Fibrocystic diseases of the liver

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Bibliographic Details
Corporate Authors: SpringerLink (Online service)
Group Author: Larson Anne M., MD.; Murray Karen F.
Published: Humana Press,
Publisher Address: [Totowa, N.J.]
Publication Dates: c2010.
Literature type: Book
Language: English
Series: Clinical gastroenterology
Subjects:
Online Access: http://dx.doi.org/10.1007/978-1-60327-524-8
Carrier Form: 1 online resource (xiv, 511 p.): ill. (some col.)
ISBN: 9781603275248 (electronic bk.)
160327524X (electronic bk.)
Index Number: R575
CLC: R575
Contents: Includes bibliographical references and index.
Embryology and development of the ductal plate / Clifford W. Bogue -- Cholangiocyte biology as relevant to cystic liver diseases / Silvia Lecchi ... [et al.] -- Cholangiocyte cilia and basal bodies / Tatyana V. Masyuk, Anatoliy I. Masyuk, and Nicholas F. LaRusso -- Genetics of fibrocystic diseases of the liver and molecular approaches to therapy / Maya Tuchman, William A. Gahl, and Meral Gunay-Aygun -- Radiologic findings in the fibrocystic diseases / Orpheus Kolokythas and Grace Phillips -- Pathology of fibrocystic diseases of the liver / Camtu D. Nguyen Truong and Matthew M. Yeh -- Alagille Syndrome and JAGGED1/NOTCH sequence / Binita M. Kamath, Kathleen M. Loomes, and David A Piccoli -- Biliary atresia and the ductal plate / Ronald J. Sokol and Cara L. Mack. Nephronophthisis and renal-hepatic-pancreatic dysplasia of Ivemark / David A. Myers and Jordan M. Symons -- Meckel and Joubert syndromes / Melissa A. Parisi, Laura S. Finn, and Ian A. Glass -- Bardet-Biedl and Jeune syndromes / Aoife M. Waters and Philip L Beales -- Congenital disorders of glycosylation and their effects on the liver / Erik A. Eklund and Hudson H. Freeze -- Autosomal recessive polycystic kidney disease / Jodi M. Smith and Ruth A. McDonald -- Caroli disease, Caroli syndrome, and Congenital hepatic fibrosis / Ronen Arnon, Henrietta Kotlus Rosenberg, and Frederick J. Suchy -- Simple hepatic cysts/choledochal cysts / André A.S. Dick and Patrick J. Healey -- Autosomal dominant polycystic liver disease / Qi Qian, Vicente E. Torres, and Stefan Somlo -- Echinococcal/Hydatid cysts of the liver / Paul S. Pottinger, Austin Spitzer, and Raymond R. Yeung -- Miscellaneous cystic lesions of the liver / Iris W. Liou -- Vascular complications of fibrocystic liver disease / Maarouf Hoteit and Patrick S. Kamath -- Biliary cystadenoma and cystadenocarcinoma / Paolo Del Poggio, Ezio Pezzica, and Daniela Corti -- Cholangitis / Shayan Irani and Richard Kozarek -- Surgical management of fibrocystic liver disease
In recent years, there have been huge advances in the understanding of the genetic and molecular basis of the fibrocystic diseases. This volume provides a thorough review of fibrocyctic diseases that affect the liver. It contains in-depth discussions of the genetics, molecular biology, pathogenesis, histology, clinical presentations, complications of, treatment, and prognosis of the conditions affecting children and adults, and hence will be the gold-standard reference for these conditions. In addition, the histological features that distinguish these conditions from other potentially fibrosin.